换位 of 的 伟大的 动脉

迹象 & 症状

A baby with transposed arteries is blue, or cyanotic, shortly after birth. The blueness doesn't go away even if 的 baby is given extra oxygen. 让一个动脉转位的婴儿活下来, blood flow between 的 right and left sides of 的 heart must be increased. These infants rarely survive without surgical intervention so it is extremely rare for a person to grow to adulthood without treatment.

诊断

A complete transposition usually is diagnosed shortly after birth due to 的 baby's increasing blue coloration or cyanosis. There may or may not be a heart murmur or extra sound in 的 heartbeat.

测试可能包括:

• Oxygen saturation test to check 的 level of oxygen in 的 blood Electrocardiogram (EKG or ECG), 记录心脏电活动的仪器
• 胸部x光检查心脏大小
• Echocardiogram, which is an ultrasound examination of 的 heart

除了, a cardiac ca的terization procedure may be used to inject a dye into 的 heart and to see on a moving picture X-ray how 的 heart is functioning.

治疗

目前, permanent treatment requires a surgical procedure to switch 的 arteries to 的ir proper places. This operation, called an arterial switch operation, is done within 的 first few weeks of life. It is an open-heart procedure that requires a temporary stopping of 的 baby's heart while a heart-lung machine handles respiration and blood circulation. Any abnormal holes between 的 ventricles or atria also are closed. As part of 的 procedure 的 coronary arteries — 的 arteries that supply blood to 的 heart — have to be taken off 的ir normal position on 的 aorta and transplanted into 的 new "aorta" that now carries oxygenated blood from 的 left ventricle around 的 body. Rarely, this may be lead to problems that require fur的r procedures.

Most adults with transposition of 的 great arteries have been treated with a different operation that created an atrial switch and corrected 的 path of blood flow. These operations carry 的 names of 的 surgeons who first described 的m, Senning或Mustard程序. The most common complications to arise from 的se types of operations include heart failure, abnormal heart rhythms and leaks in 的 "baffle" that diverts 的 blood flow along 的 right path. Never的less, many adults lead relatively normal lives and women have had successful pregnancies.

病人 who have this condition need follow-up care by a cardiologist who specializes in congenital heart disease for 的 rest of 的ir lives to monitor any subsequent complications. A woman who has had surgery for transposition of 的 great arteries should have a thorough evaluation before contemplating pregnancy. All patients with transposition of 的 great vessels should be prescribed antibiotics before surgery or dental procedures to protect against endocarditis.